Rare Abstarct of Tetralogy of Fallot and Hypertrophic Cardiomyopathy in a Cyanotic infant

Tetralogy of Fallot is the most common form of cyanotic congenital heart disease. It is often associated with other congenital but its association with hypertrophic cardiomyopathy (HCM) is rarely reported. We reported a case with TOF and HCMP. Case: The case is a 6 months age male infant who admitted for treatment of TOF in Shahid Rajaee Heart Hospital Tehran. He had cyanosis and mild clubbing, vital sign was stable, weight was 6kg, Height 63 cm,HB=12,O2 saturation was 65%. Heart auscultation showed S1 was normal S2 was single with a 3/6 systolic murmur. EKG was normal sinus rhythm and right axis deviation, in CXR the CTR increase and PVM was decreased.Evaluation by echo reveal he had TOF (overriding of Aorta,sub aortic VSD,RVH,sever valaval and sub valvar pulmonary stenosis) with sever hypertrophy of LV walls (IVS diameter was 13mm,z scor= 13) Finally a right Gore tex shunt created and the general condition of patient became better and discharged. Conclusion: In patients with association of Tetralogy of Fallot (TF) and Hypertrophic Cardiomyopathy (HCM) a surgical procedure that used to increase pulmonary blood flow for palliation has better results than total correction.

کلیدواژه ها:

hypertrophic cardiomyopathy ، tetralogy of Fallot ، cyanotic infant