Disseminated Metastasis after Resection of Sacrococcygeal Teratoma with Mucinous Adenocarcinoma: A Case Report

  • سال انتشار: 1402
  • محل انتشار: مجله سرطان خاورمیانه، دوره: 14، شماره: 4
  • کد COI اختصاصی: JR_MISJ-14-4_012
  • زبان مقاله: انگلیسی
  • تعداد مشاهده: 71
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نویسندگان

Khadiga Ali

Pathology Department, Faculty of Medicine, Mansoura University, Mansoura, Egypt

Mie Ali

Pathology Department, Faculty of Medicine, Mansoura University, Mansoura, Egypt

Ramy Abbas

Medical Oncology Unit, Oncology Center Mansoura University (OCMU), Mansoura, Egypt

Ahmed Abdallah

Surgical Oncology Department, Oncology Center Mansoura University (OCMU), Mansoura, Egypt

Ahmed Seteet

Surgical Oncology Department, Oncology Center Mansoura University (OCMU), Mansoura, Egypt

Mohamed Daoud

Clinical Oncology and Nuclear Medicine Department, Mansoura University Hospital, Mansoura, Egypt

Islam Metwally

Surgical Oncology Department, Oncology Center Mansoura University (OCMU), Mansoura, Egypt

چکیده

Mature teratoma is a common tumor that can undergo malignant transformation, either in ovarian or extragonadal sites. While adenocarcinoma superimposed on sacrococcygeal teratoma is rare, mucinous variants have been reported in only five cases. Here, we present a case of a young girl with disseminated metastasis of mucinous carcinoma, initially of unknown primary origin. Further investigation by a dedicated multidisciplinary team (MDT) revealed a focus of mucinous carcinoma (intestinal type) in a sacrococcygeal teratoma incompletely resected five years earlier. The patient is currently undergoing second-line chemotherapy after experiencing side-effects on the first-line regimen. Pathologists, gynecologic oncologists, and surgical oncologists should exercise caution when dealing with locally aggressive teratomas, thoroughly searching for malignant components and conducting short-term follow-up.

کلیدواژه ها

Teratoma, Adenocarcinoma, Mucinous, Unknown primary, Sacrococcygeal

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