Primary Huge Retroperitoneal Mucinous Cystadenoma in an Iranian Woman : A Case Report

IntroductionPrimary retroperitoneal mucinous cystadenoma is a rare tumor among women. Herein, we present a 47-year-old Iranian woman complaining of abdominal discomfort for six months. Case presentationThe patient and her family had always lived an urban life and they didn’t have any close contact with farm animals and their products. She didn’t mention any history of malignant or benign abdominal tumors in her first-degree relatives. The primary evaluation showed normal lab data but a huge retroperitoneal cyst in imaging studies. The patient underwent exploratory laparotomy. A 19x14x8 cm well-defined cystic lesion with mild adhesion to the lower pole of the left kidney and descending colon was noticed. The mass was dissected from the adjacent organs and removed completely without spillage of its content. The histopathologic evaluation of the cyst was compatible with retroperitoneal mucinous cystadenoma. Three years’ follow-up did not show any recurrence of the tumor. To our knowledge, less than 50 cases with this pathology have been reported and published in the literature and this case is the second one in Iran. ConclusionsAlthough primary retroperitoneal mucinous cystadenoma is a very rare entity, it should be considered in the differential diagnosis of any retroperitoneal cystic lesion. Since the definitive diagnosis of these lesions is made by histopathologic evaluation, complete resection of them is both diagnostic and therapeutic.

کلیدواژه ها:

Retroperitoneal cyst ، cystadenoma ، mucinous ، case reports